Idiopathic pulmonary hemosiderosis complicated by Down syndrome
Identifieur interne : 000F51 ( Main/Exploration ); précédent : 000F50; suivant : 000F52Idiopathic pulmonary hemosiderosis complicated by Down syndrome
Auteurs : Hirofumi Watanabe [Japon] ; Mamoru Ayusawa [Japon] ; Masataka Kato [Japon] ; Ami Chou [Japon] ; Akiko Komori [Japon] ; Yuriko Abe [Japon] ; Masaharu Matsumura [Japon] ; Hiroshi Kamiyama [Japon] ; Hiroyuki Izumi [Japon] ; Shori Takahashi [Japon]Source :
- Pediatrics International [ 1328-8067 ] ; 2015-10.
Abstract
We report the case of a 9‐year‐old girl with Down syndrome (DS) diagnosed with idiopathic pulmonary hemosiderosis (IPH). Although acute pneumonia complicated by hemolytic anemia was suspected, IPH was finally diagnosed on bronchoscopy. Treatment with prednisolone achieved good clinical response. An association between IPH and DS was not able to be identified, but immunological issues in DS may contribute to the onset of IPH. Recurrent and intractable respiratory symptoms with marked infiltrative shadows in the bilateral lungs and complicated by severe anemia in patients with DS should suggest IPH.
Url:
DOI: 10.1111/ped.12690
Affiliations:
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<front><div type="abstract">We report the case of a 9‐year‐old girl with Down syndrome (DS) diagnosed with idiopathic pulmonary hemosiderosis (IPH). Although acute pneumonia complicated by hemolytic anemia was suspected, IPH was finally diagnosed on bronchoscopy. Treatment with prednisolone achieved good clinical response. An association between IPH and DS was not able to be identified, but immunological issues in DS may contribute to the onset of IPH. Recurrent and intractable respiratory symptoms with marked infiltrative shadows in the bilateral lungs and complicated by severe anemia in patients with DS should suggest IPH.</div>
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